Amyloid infiltration of the diaphragm as a cause of respiratory failure.
نویسندگان
چکیده
Respiratory involvement with amyloidosis typically involves the tracheobronchial tree or lung parenchyma. We describe a patient with systemic amyloidosis who was respirator-dependent because of extensive amyloid infiltration of the diaphragm, with no evidence of other pulmonary amyloidosis. Diaphragmatic myopathy from amyloid should be considered in respiratory failure in amyloidosis.
منابع مشابه
Amyloid myopathy presenting with respiratory failure.
Amyloidosis is a rare cause of myopathy. Its prominent or presenting feature may be respiratory failure. Physiological measurement of transdiaphragmatic pressure and biopsy specimens of muscle show the pathological mechanism to be diaphragm weakness due to amyloid infiltration of the diaphragm rather than parenchymal lung involvement. Thus amyloid myopathy even without the typical macroglossia ...
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ورودعنوان ژورنال:
- Chest
دوره 89 5 شماره
صفحات -
تاریخ انتشار 1986